A 59-year-old woman presents with syncope. With a family history of sudden cardiac death, her workup for ventricular tachycardia reveals a serious finding.
A 59-year-old woman was admitted to the hospital with unheralded syncope. She had lost a son to sudden cardiac death when he was 29 years of age. On hospital day 2, the patient developed sustained monomorphic ventricular tachycardia treated with synchronized cardioversion and intravenous amiodarone. An electrocardiogram was performed after the event (Panel A). A transesophageal echocardiogram showed a severely dilated right ventricle (Panel B). Cardiac magnetic resonance imaging showed a right ventricular ejection fraction of 27% with regional akinesis. What is the most likely diagnosis?
What is the most likely diagnosis?
Arrhythmogenic right ventricular cardiomyopathy, Epsilon Wave, Sudden Cardiac Death, Syncope, Ventricular Tachycardia
