A 54-year-old man presents with a 3-week history of cognitive decline, Ataxia, and myoclonus. Explore the diagnosis of this rapidly fatal condition.
A 54-year-old man presented with a 3-week history of cognitive deterioration. Neurologic examination revealed disorientation, horizontal gaze-evoked nystagmus, hyperreflexia, startle myoclonus, and ataxia. Brain MRI with diffusion-weighted imaging revealed hyperintensity of the cortical gyri and caudate heads. What is the diagnosis?
What is the most likely diagnosis?
Creutzfeld-Jakob disease, MRI, Myoclonus, Prion Disease, Rapidly Progressive Dementia
